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| ====== Ohtahara syndrome ====== | ====== Ohtahara syndrome ====== |
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| [{{ :content:ohtahara.jpg?direct&100|Shunsuke Ohtahara [1930-2013]}}]Ohtahara syndrome is a rare electroclinical epilepsy syndrome with onset in the neonatal period. It is also known as [[early infantile epileptic encephalopathy]] (EIEE) or early infantile epileptic encephalopathy with burst suppression pattern. It is named after [[Shunsuke Ohtahara]], the Japanese child neurologist who first described the syndrome in 1976 [(:cite:Ohtahara1976>Ohtahara, S. et al. No To Hattatsu. 1976; 8: 270–280)]. | [{{ :content:ohtahara.jpg?direct&100|Shunsuke Ohtahara [1930-2013]}}]Ohtahara syndrome is a rare electroclinical epilepsy syndrome with onset in the neonatal period. It is also known as [[early infantile epileptic encephalopathy]] (EIEE) or early infantile epileptic encephalopathy with burst suppression pattern. It is named after [[Shunsuke Ohtahara]], the Japanese child neurologist who first described the syndrome in 1976 [(:cite:Ohtahara1976>Ohtahara, S. et al. No To Hattatsu. 1976; 8: 270–280)]. |
| ===== Epidemiology ===== | ===== Epidemiology ===== |
| * Ohtahara syndrome can evolve to [[West syndrome]] and then to [[Lennox-Gastaut syndrome]], or can transition to severe focal epilepsy | * Ohtahara syndrome can evolve to [[West syndrome]] and then to [[Lennox-Gastaut syndrome]], or can transition to severe focal epilepsy |
| * High incidence of mortality & morbidity with permanent cognitive and neurologic deficits | * High incidence of mortality & morbidity with permanent cognitive and neurologic deficits |
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| ===== Differential Diagnosis ===== | ===== Differential Diagnosis ===== |
| * [[early myoclonic encephalopathy]]. <noprint>See [[neurolists:differentiating_between_ohtahara_syndrome_early_myoclonic_encephalopathy]].</noprint> | * [[early myoclonic encephalopathy]]. <noprint>See [[neurolists:differentiating_between_ohtahara_syndrome_early_myoclonic_encephalopathy]].</noprint> |
