content:acycarnitines

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Acylcarnitines

Acute myopathy, rhabdomyolysis. Unexplained increased creatine kinase

  • serum acylcarnitines are useful in the diagnosis of fatty acid oxidation disorders and several organic acidurias
  • also useful in evaluating treatment during follow-up of patients with fatty acid beta-oxidation disorders and several organic acidurias
  • specific acylcarnitines indicate particular disorders, e.g. octanoyl carnitine in MCAD deficiency, glutaryl carnitine in GA1, propionyl carnitine in cobalamin disorders
< or =7 days (nmol/mL) < or =7 days (nmol/mL)
8 days-7 years 8 days-7 years
(nmol/mL) (nmol/mL)
> or =8 years > or =8 years
(nmol/mL) (nmol/mL)
Acetylcarnitine, C2 Acetylcarnitine, C2
2.14-15.89 2.14-15.89
2.00-27.57 2.00-27.57
2.00-17.83 2.00-17.83
Acrylylcarnitine, C3:1 Acrylylcarnitine, C3:1
<0.04 <0.04
<0.05 <0.05
<0.07 <0.07
Propionylcarnitine, C3 Propionylcarnitine, C3
<0.55 <0.55
<1.78 <1.78
<0.88 <0.88
Formiminoglutamate, FIGLU Formiminoglutamate, FIGLU
<0.43 <0.43
<0.08 <0.08
<0.14 <0.14
Iso-/Butyrylcarnitine, C4 Iso-/Butyrylcarnitine, C4
<0.46 <0.46
<1.06 <1.06
<0.83 <0.83
Tiglylcarnitine, C5:1 Tiglylcarnitine, C5:1
<0.05 <0.05
<0.09 <0.09
<0.11 <0.11
Isovaleryl-/2-Methylbutyrylcarn C5 Isovaleryl-/2-Methylbutyrylcarn C5
<0.38 <0.38
<0.63 <0.63
<0.51 <0.51
3-OH-iso-/butyrylcarnitine, C4-OH 3-OH-iso-/butyrylcarnitine, C4-OH
<0.13 <0.13
<0.51 <0.51
<0.18 <0.18
Hexenoylcarnitine, C6:1 Hexenoylcarnitine, C6:1
<0.12 <0.12
<0.10 <0.10
<0.15 <0.15
Hexanoylcarnitine, C6 Hexanoylcarnitine, C6
<0.14 <0.14
<0.23 <0.23
<0.17 <0.17
3-OH-isovalerylcarnitine, C5-OH 3-OH-isovalerylcarnitine, C5-OH
<0.08 <0.08
<0.12 <0.12
<0.10 <0.10
Benzoylcarnitine Benzoylcarnitine
<0.13 <0.13
<0.07 <0.07
<0.10 <0.10
Heptanoylcarnitine, C7 Heptanoylcarnitine, C7
<0.05 <0.05
<0.05 <0.05
<0.06 <0.06
3-OH-hexanoylcarnitine, C6-OH 3-OH-hexanoylcarnitine, C6-OH
<0.08 <0.08
<0.19 <0.19
<0.09 <0.09
Phenylacetylcarnitine Phenylacetylcarnitine
<0.15 <0.15
<0.22 <0.22
<0.29 <0.29
Salicylcarnitine Salicylcarnitine
<0.08 <0.08
<0.09 <0.09
<0.09 <0.09
Octenoylcarnitine, C8:1 Octenoylcarnitine, C8:1
<0.48 <0.48
<0.91 <0.91
<0.88 <0.88
Octanoylcarnitine, C8 Octanoylcarnitine, C8
<0.19 <0.19
<0.45 <0.45
<0.78 <0.78
Malonylcarnitine, C3-DC Malonylcarnitine, C3-DC
<0.09 <0.09
<0.14 <0.14
<0.26 <0.26
Decadienoylcarnitine, C10:2 Decadienoylcarnitine, C10:2
<0.11 <0.11
<0.12 <0.12
<0.26 <0.26
Decenoylcarnitine, C10:1 Decenoylcarnitine, C10:1
<0.25 <0.25
<0.46 <0.46
<0.47 <0.47
Decanoylcarnitine, C10 Decanoylcarnitine, C10
<0.27 <0.27
<0.91 <0.91
<0.88 <0.88
Methylmalonyl-/succinylcarn, C4-DC Methylmalonyl-/succinylcarn, C4-DC
<0.05 <0.05
<0.05 <0.05
<0.05 <0.05
3-OH-decenoylcarnitine, C10:1-OH 3-OH-decenoylcarnitine, C10:1-OH
<0.12 <0.12
<0.12 <0.12
<0.13 <0.13
Glutarylcarnitine, C5-DC Glutarylcarnitine, C5-DC
<0.06 <0.06
<0.10 <0.10
<0.11 <0.11
Dodecenoylcarnitine, C12:1 Dodecenoylcarnitine, C12:1
<0.19 <0.19
<0.37 <0.37
<0.35 <0.35
Dodecanoylcarnitine, C12 Dodecanoylcarnitine, C12
<0.18 <0.18
<0.35 <0.35
<0.26 <0.26
3-Methylglutarylcarnitine, C6-DC 3-Methylglutarylcarnitine, C6-DC
<0.28 <0.28
<0.21 <0.21
<0.43 <0.43
3-OH-dodecenoylcarnitine, C12:1-OH 3-OH-dodecenoylcarnitine, C12:1-OH
<0.11 <0.11
<0.10 <0.10
<0.13 <0.13
3-OH-dodecanoylcarnitine, C12-OH 3-OH-dodecanoylcarnitine, C12-OH
<0.06 <0.06
<0.09 <0.09
<0.08 <0.08
Tetradecadienoylcarnitine, C14:2 Tetradecadienoylcarnitine, C14:2
<0.09 <0.09
<0.13 <0.13
<0.18 <0.18
Tetradecenoylcarnitine, C14:1 Tetradecenoylcarnitine, C14:1
<0.16 <0.16
<0.35 <0.35
<0.24 <0.24
Tetradecanoylcarnitine, C14 Tetradecanoylcarnitine, C14
<0.11 <0.11
<0.15 <0.15
<0.12 <0.12
Octanedioylcarnitine, C8-DC Octanedioylcarnitine, C8-DC
<0.25 <0.25
<0.19 <0.19
<0.19 <0.19
3-OH-tetradecenoylcarnitine C14:1OH 3-OH-tetradecenoylcarnitine C14:1OH
<0.06 <0.06
<0.18 <0.18
<0.13 <0.13
3-OH-tetradecanoylcarnitine, C14-OH 3-OH-tetradecanoylcarnitine, C14-OH
<0.04 <0.04
<0.05 <0.05
<0.08 <0.08
Hexadecenoylcarnitine, C16:1 Hexadecenoylcarnitine, C16:1
<0.15 <0.15
<0.21 <0.21
<0.10 <0.10
Hexadecanoylcarnitine, C16 Hexadecanoylcarnitine, C16
<0.36 <0.36
<0.52 <0.52
<0.23 <0.23
3-OH-hexadecenoylcarnitine,C16:1-OH 3-OH-hexadecenoylcarnitine,C16:1-OH
<0.78 <0.78
<0.36 <0.36
<0.06 <0.06
3-OH-hexadecanoylcarnitine, C16-OH 3-OH-hexadecanoylcarnitine, C16-OH
<0.10 <0.10
<0.07 <0.07
<0.06 <0.06
Octadecadienoylcarnitine, C18:2 Octadecadienoylcarnitine, C18:2
<0.12 <0.12
<0.31 <0.31
<0.24 <0.24
Octadecenoylcarnitine, C18:1 Octadecenoylcarnitine, C18:1
<0.25 <0.25
<0.45 <0.45
<0.39 <0.39
Octadecanoylcarnitine, C18 Octadecanoylcarnitine, C18
<0.10 <0.10
<0.12 <0.12
<0.14 <0.14
Dodecanedioylcarnitine, C12-DC Dodecanedioylcarnitine, C12-DC
<0.10 <0.10
<0.04 <0.04
<0.04 <0.04
3-OH-octadecadienoylcarn, C18:2-OH 3-OH-octadecadienoylcarn, C18:2-OH
<0.04 <0.04
<0.06 <0.06
<0.06 <0.06
3-OH-octadecenoylcarnitine C18:1-OH 3-OH-octadecenoylcarnitine C18:1-OH
<0.03 <0.03
<0.04 <0.04
<0.06 <0.06
3-OH-octadecanoylcarnitine, C18-OH 3-OH-octadecanoylcarnitine, C18-OH
<0.03 <0.03
<0.05 <0.05
<0.03 <0.03
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  • content/acycarnitines.1581875094.txt.gz
  • Last modified: 2020/02/16 17:44
  • by icna