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Acute disseminated encephalomyelitis (ADEM) in children: a multicenter retrospective study

Objectives: To present demographic, clinical, laboratory and prognostic data in a large group of children with ADEM and to investigate the role of anti-MOG antibodies in clinical findings and outcome. Methods: ADEM patients (n=245) from 24 centers diagnosed in 2010-2021were retrospectively evaluated with descriptive statistics. Duplicate cases were excluded. Results: The male/female ratio was 1.66:1, mean age at diagnosis was 6.33.8 (0.5-17.7) years. The most common findings on admission besides altered state of consciousness were fatigue (57.1%), headache (40.4%), and fever (39.6%). Serum anti-MOG antibodies were tested in 84 patients and 27 (32%) found positive by cell-based assay. Anti-MOG-positive patients were younger (5.12.7 vs. 7.13.4) and their blood white blood cell count was higher (15,1006,116/mm3 vs. 12,1685,830/mm3). Twenty-three (9.4%) patients had relapses. The final diagnoses and their anti-MOG antibody status is given in Table-1. Anti-MOG antibody positivity was not associated with need for intensive care unit, relapse, or recovery. Among the 172 patients with at least one-year follow-up, Glasgow Coma Score <10, need for intensive care unit, mechanical ventilation, and the presence of seizures on admission were associated with incomplete recovery [Modified Rankin Score (mRS)1 (n=26), epilepsy (n=20), (p<0.005)]. Only three patients (1,7%) remained dependent [mRS=3 (n=1), mRS=4 (n=2)] at one-year of follow-up. Conclusion: ADEM is usually monophasic with relapses in 10% of the patients. The overall prognosis is good, regardless of the anti-MOG antibody status. The clinical condition on admission appeared as the most important prognostic factor.
Keywords: Acute disseminated encephalomyelitis, anti-MOG antibodies

Seda Kanmaz
Ege University Medical Faculty
Turkey

Sanem Yilmaz
Ege University Medical Faculty
Turkey

Nihal Olgac Dündar
Izmir Katip Celebi University Faculty of Medicine
Turkey

Ayse Aksoy
Ondokuz Mayis University Medical Faculty
Turkey

Mehmet Canpolat
Erciyes University Medical Faculty
Turkey

Huseyin Per
Erciyes University Medical Faculty
Turkey

Ilknur Erol
Baskent University Faculty of Medicine, Adana Dr.Turgut Noyan Application and Research Center
Turkey

Hakan Gumus
Erciyes University Medical Faculty
Turkey

Yasemin Ozkale
Baskent University Faculty of Medicine, Adana Dr.Turgut Noyan Application and Research Center
Turkey

Selcan Ozturk
Erciyes University Medical Faculty
Turkey

Dilara Ece Toprak
Ege University Medical Faculty
Turkey

Ibrahim Oncel
Hacettepe University Medical Faculty
Turkey

Murat Ozkale
Baskent University Faculty of Medicine, Adana Dr.Turgut Noyan Application and Research Center
Turkey

Elif Nurdan Mansur
Erciyes University Medical Faculty
Turkey

Hepsen Mine Serin
Ege University Medical Faculty
Turkey

Gulsen Ersoz
Hacettepe University Medical Faculty
Turkey

Seyda Besen
Baskent University Faculty of Medicine, Adana Dr.Turgut Noyan Application and Research Center
Turkey

Gulen Gul Mert
Cukurova University Medical Faculty
Turkey

Ayten Gulec
Erciyes University Medical Faculty
Turkey

Sevim Sahin
Karadeniz Technical University Medical Faculty
Turkey

Cemile Busra Olculu
Ege University Medical Faculty
Turkey

Ayberk Selek
Hacettepe University Medical Faculty
Turkey

Serdar Pekuz
University of Health Sciences Dr. Behçet Uz Child Disease and Pediatric Surgery Training and Research Hospital
Turkey

Gunce Basarir
University of Health Sciences Tepecik Training and Research Hospital
Turkey

Cagatay Gunay
Dokuz Eylul University Medical Faculty
Turkey

Leman Tekin Orgun
Baskent University Faculty of Medicine, Adana Dr.Turgut Noyan Application and Research Center
Turkey

Didem Bİcer
Cukurova University Medical Faculty
Turkey

Zehra Filiz Kahraman
Erciyes University Medical Faculty
Turkey

Deniz Yuksel
University of Health Sciences Turkey, Dr. Sami Ulus Research and Training Hospital
Turkey

Meral Karadag
Inonu University Medical Faculty
Turkey

Erdem Simsek
Ege University Medical Faculty
Turkey

Aycan Unalp
University of Health Sciences Dr. Behçet Uz Child Disease and Pediatric Surgery Training and Research Hospital
Turkey

Nihal Yildiz
Karadeniz Technical University Medical Faculty
Turkey

Meltem Cobanogullari Direk
Mersin University Medical Faculty
Turkey

Uluc Yis
Dokuz Eylul University Medical Faculty
Turkey

Huseyin Tan
Ataturk University Medical Faculty
Turkey

Cengiz Havali
Bursa Yuksek İhtisas Training and Research Hospital
Turkey

Aydan Degerliyurt

Turkey

Mesut Gungor
Kocaeli University Medical Faculty
Turkey

Ozlem Herguner
Cukurova University Medical Faculty
Turkey

Elif Perihan Oncel
Baskent University Faculty of Medicine, Adana Dr.Turgut Noyan Application and Research Center
Turkey

Olcay Unver
Marmara University Medical Faculty
Turkey

Hale Atalay Celik
University of Health Sciences Turkey, Dr. Sami Ulus Research and Training Hospital
Turkey

Bilge Ozgor
Inonu University Medical Faculty
Turkey

Ali Cansu
Karadeniz Technical University Medical Faculty
Turkey

Asli Kubra Atasever
Celal Bayar University Medical Faculty
Turkey

Ayse Tosun
Adnan Menderes University Medical Faculty
Turkey

Olcay Gungor
Pamukkale University Medical Faculty
Turkey

Cetin Okuyaz
Mersin University Medical Faculty
Turkey

Selvinaz Edizer
Bezm-i Alem Vakif University Medical Faculty
Turkey

Semra Hız
Dokuz Eylul University Medical Faculty
Turkey

Esra Sarıgecili
Adana City Training and Research Hospital
Turkey

Gokcen Oz Tuncer
Ondokuz Mayis University Medical Faculty
Turkey

Pinar Gencpinar
Izmir Katip Celebi University Faculty of Medicine
Turkey

Unsal Yilmaz
University of Health Sciences Dr. Behçet Uz Child Disease and Pediatric Surgery Training and Research Hospital
Turkey

Hasan Tekgul
Ege University Medical Faculty
Turkey

Banu Anlar
Hacettepe University Medical Faculty
Turkey

 

 


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